Non-cirrhotic portal hypertension: A possibly benign but complicated disease
نویسندگان
چکیده
منابع مشابه
Idiopathic non-cirrhotic portal hypertension
Idiopathic non-cirrhotic portal hypertension Sith Siramolpiwat1,2, Susana Seijo3* 1Chulabhorn International College of Medicine, Thammasat University, Pathumthani, 12120, Thailand 2Division of Gastroenterology, Department of Internal Medicine, Faculty of Medicine, Thammasat University, Pathumthani, 12120, Thailand 3CTO, Department of Medicine, Icahn School of Medicine at Mount Sinai, New York, ...
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Idiopathic non-cirrhotic portal hypertension (INCPH) is a rare disease characterized of intrahepatic portal hypertension in the absence of cirrhosis or other causes of liver disease and splanchnic venous thrombosis. The etiology of INCPH can be classified in five categories: 1) immunological disorders (i.e. association with common variable immunodeficiency syndrome, connective tissue diseases, ...
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Renal glomerular changes are a well recognised complication of cirrhosis and are frequently characterised by mesangial IgA deposition. We report a patient with non-cirrhotic portal hypertension who developed IgA nephropathy and a nephrotic syndrome with renal histological changes classically associated with cirrhosis. Splenectomy with resection of a splenic artery aneurysm resulted in remission...
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Liver cirrhosis but also portal vein obstruction cause portal hypertension (PHT) and angiogenesis. This study investigated the differences of angiogenesis in cirrhotic and non-cirrhotic PHT with special emphasis on the canonical (Shh/Gli) and non-canonical (Shh/RhoA) hedgehog pathway. Cirrhotic (bile duct ligation/BDL; CCl4 intoxication) and non-cirrhotic (partial portal vein ligation/PPVL) rat...
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ژورنال
عنوان ژورنال: Digestive and Liver Disease
سال: 2018
ISSN: 1590-8658
DOI: 10.1016/j.dld.2018.05.018